Mandibular reconstruction in patients with familial gigantiform cementoma: report of 2 cases and review of the literature

Abstract

Abstract: Familial gigantiform cementoma (FGC) is a rare autosomal dominant, benign fibro-cementoosseous lesion that is generally limited to the facial bones, typically in the anterior portion of the mandible. The treatment remains extensive resection with reconstruction of the osseous defect to provide aesthetic and functional rehabilitation. However, patients with FGC often have concomitant long bone abnormalities and pubertal pathologic fractures. In addition, FGC always presents in the first or second decades. Therefore, the choice of bone reconstruction warrants extreme caution. Literatures regarding the treatment of such patients are limited. This paper reported 2 patients with FGC treated at our hospital. Postoperative appearance, oral function and radiographic images were evaluated. The treatment experience was summarized based on review of relevant literatures.

Key words: Familial gigantiform cementoma, Mandible reconstruction, Long bone fracture, Vascularized iliac crest free flap

CLC Number:

R739.8

WANG Hong-wei, MA Chun-yue, HE Guang, XU Li-qun, ZHANG Chen-ping, QIN Xing-jun. Mandibular reconstruction in patients with familial gigantiform cementoma: report of 2 cases and review of the literature[J]. China Journal of Oral and Maxillofacial Surgery, 2016, 14(1): 89-92.

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