Diagnosis, treatment and prognosis of alveolar soft part sarcoma of the head and neck region

Abstract

Abstract: Alveolar soft part sarcoma (ASPS) is an extremely rare malignant neoplasm that accounts for less than 1% of all soft tissue sarcomas. Despite being a slow-growing tumor with an asymptomatic course, ASPS demonstrates a disproportionate frequency of distant metastases even at the early stages of disease. The delay of diagnosis brings about many difficulties to obtain a more favorable clinical course. Recently, owing to the development of technique, the diagnosis and treatment progress of ASPS continue to improve. This paper summarized the literatures on diagnosis, treatment progress and prognosis of ASPS of the head and neck region.

Key words: Alveolar soft part sarcoma, Head and neck region, Sarcoma

CLC Number:

R739.8

WANG Hong-wei, WANG Xu-kai, QIN Xing-jun, ZHANG Chen-ping. Diagnosis, treatment and prognosis of alveolar soft part sarcoma of the head and neck region[J]. China Journal of Oral and Maxillofacial Surgery, 2016, 14(3): 276-281.

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